Sturge Weber Syndrome. A rare experience at Liaquat University of Medical & Health Sciences, Jamshoro
Dr. Bilal Fazal Shaikh
Objective: To evaluate the incidence of Sturge Weber Syndrome at Department of Plastic & Reconstructive Surgery, LUMHS, Jamshoro/ Hyderabad.
Study design: Descriptive case series.
Patients & Methods: This study was done on patients who were presented with Sturge Weber syndrome at the Department of Plastic & Reconstructive Surgery, Liaquat University of Medical & Health Sciences, Jamshoro / Hyderabad from 2000 to 2007. Follow up included assessment of reconstructive procedures performed, presence of infection and aesthetic balance.
12 cases of SWS included 5 males and 7 females. Surgical treatment was offered in nine cases. In six patients defect was closed by primary closure and cheek rotation flap was performed on 3 patients. At follow-up all patients had improved appearance with resultant contented mood and improved self confidence. Reduction in the drooping of the cheek and lips resulted in a competent oral sphincter and cessation of the dribbling of the saliva. It also helped in prevention of development of future complications like mucosal ulceration, infection and hemorrhage.
CONCLUSION: Sturge-Weber syndrome engrosses specific problems that need to be considered. Sturge-Weber syndrome is clinically important to the Plastic Surgeons because of its associated facial vascular features and their complicating manifestations. Periodic evaluation and examinations are recommended to identify and prevent any complications secondary to reconstruction.
Key words: Sturge Weber syndrome, Port wine stain, venous abnormality, rotation flap.